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  • Merrill Benson
2020

Editorial Commentary: Advances in transthyretin amyloid cardiomyopathy

Benson, M. D. & Dasgupta, N. R., Jan 1 2020, (Accepted/In press) In : Trends in Cardiovascular Medicine.

Research output: Contribution to journalEditorial

Inotersen preserves or improves quality of life in hereditary transthyretin amyloidosis

Coelho, T., Yarlas, A., Waddington-Cruz, M., White, M. K., Sikora Kessler, A., Lovley, A., Pollock, M., Guthrie, S., Ackermann, E. J., Hughes, S. G., Karam, C., Khella, S., Gertz, M., Merlini, G., Obici, L., Schmidt, H. H., Polydefkis, M., Dyck, P. J. B., Brannagan, T. H., Conceição, I. & 2 others, Benson, M. D. & Berk, J. L., Apr 1 2020, In : Journal of neurology. 267, 4, p. 1070-1079 10 p.

Research output: Contribution to journalArticle

Open Access

Inotersen therapy of transthyretin amyloid cardiomyopathy

Dasgupta, N. R., Rissing, S. M., Smith, J., Jung, J. & Benson, M. D., Jan 2 2020, In : Amyloid. 27, 1, p. 52-58 7 p.

Research output: Contribution to journalArticle

2019

A cell-based high-throughput screening method to directly examine transthyretin amyloid fibril formation at neutral pH

Ueda, M., Okada, M., Mizuguchi, M., Kluve-Beckerman, B., Kanenawa, K., Isoguchi, A., Misumi, Y., Tasaki, M., Ueda, A., Kanai, A., Sasaki, R., Masuda, T., Inoue, Y., Nomura, T., Shinriki, S., Shuto, X. T., Kai, H., Yamashita, T., Matsui, H., Benson, M. D. & 1 others, Ando, Y., Jul 19 2019, In : Journal of Biological Chemistry. 294, 29, p. 11259-11275 17 p.

Research output: Contribution to journalArticle

Open Access
1 Scopus citations

ALECT2 and NASH

Cummings, O., Dasgupta, N. & Benson, M., Mar 29 2019, In : Amyloid. 26, sup1, p. 158-159 2 p.

Research output: Contribution to journalLetter

A pair of peptides inhibits seeding of the hormone transporter transthyretin into amyloid fibrils

Saelices, L., Nguyen, B. A., Chung, K., Wang, Y., Ortega, A., Lee, J. H., Coelho, T., Bijzet, J., Benson, M. D. & Eisenberg, D. S., Apr 12 2019, In : Journal of Biological Chemistry. 294, 15, p. 6130-6141 12 p.

Research output: Contribution to journalArticle

Open Access
4 Scopus citations

A transgenic mouse model reproduces human hereditary systemic amyloidosis

Chabert, M., Rousset, X., Colombat, M., Lacasa, M., Kakanakou, H., Bourderioux, M., Brousset, P., Burlet-Schiltz, O., Liepnieks, J. J., Kluve-Beckerman, B., Lambert, G., Châtelet, F. P., Benson, M. D. & Kalopissis, A. D., Sep 2019, In : Kidney international. 96, 3, p. 628-641 14 p.

Research output: Contribution to journalArticle

5 Scopus citations

Inotersen treatment for ATTR amyloidosis

Benson, M., Mar 29 2019, In : Amyloid. 26, sup1, p. 27-28 2 p.

Research output: Contribution to journalLetter

Treatment of ATTR cardiomyopathy with a TTR specific antisense oligonucleotide, inotersen

Dasgupta, N. R. & Benson, M. D., Mar 29 2019, In : Amyloid. 26, sup1, p. 20-21 2 p.

Research output: Contribution to journalLetter

2018

Amyloid nomenclature 2018: recommendations by the International Society of Amyloidosis (ISA) nomenclature committee

Benson, M. D., Buxbaum, J. N., Eisenberg, D. S., Merlini, G., Saraiva, M. J. M., Sekijima, Y., Sipe, J. D. & Westermark, P., Oct 2 2018, In : Amyloid. 25, 4, p. 215-219 5 p.

Research output: Contribution to journalArticle

69 Scopus citations

Amyloid seeding of transthyretin by ex vivo cardiac fibrils and its inhibition

Saelices, L., Chung, K., Lee, J. H., Cohn, W., Whitelegge, J. P., Benson, M. D. & Eisenberg, D. S., Jul 17 2018, In : Proceedings of the National Academy of Sciences of the United States of America. 115, 29, p. E6741-E6750

Research output: Contribution to journalArticle

8 Scopus citations

Hereditary transthyretin amyloidosis: baseline characteristics of patients in the NEURO-TTR trial

Waddington-Cruz, M., Ackermann, E. J., Polydefkis, M., Heitner, S. B., Dyck, P. J., Barroso, F. A., Wang, A. K., Berk, J. L., Dyck, P. J. B., Monia, B. P., Hughes, S. G., Tai, L., Jesse Kwoh, T., Jung, S. W., Coelho, T., Benson, M. D. & Gertz, M. A., Jul 3 2018, In : Amyloid. 25, 3, p. 180-188 9 p.

Research output: Contribution to journalArticle

6 Scopus citations

Inotersen treatment for patients with Hereditary transthyretin amyloidosis

Benson, M. D., Waddington-Cruz, M., Berk, J. L., Polydefkis, M., Dyck, P. J., Wang, A. K., Planté-Bordeneuve, V., Barroso, F. A., Merlini, G., Obici, L., Scheinberg, M., Brannagan, T. H., Litchy, W. J., Whelan, C., Drachman, B. M., Adams, D., Heitner, S. B., Conceição, I., Schmidt, H. H., Vita, G. & 15 others, Campistol, J. M., Gamez, J., Gorevic, P. D., Gane, E., Shah, A. M., Solomon, S. D., Monia, B. P., Hughes, S. G., Jesse Kwoh, T., McEvoy, B. W., Jung, S. W., Baker, B. F., Ackermann, E. J., Gertz, M. A. & Coelho, T., Jul 5 2018, In : New England Journal of Medicine. 379, 1, p. 22-31 10 p.

Research output: Contribution to journalArticle

241 Scopus citations
2017

AA cardiomyopathy

Dasgupta, N., Cummings, O., Phillips, C. & Benson, M., Mar 16 2017, In : Amyloid. 24, p. 138-139 2 p.

Research output: Contribution to journalLetter

An aggressive form of transthyretin amyloidosis

Dasgupta, N., Wang, A. K., Hardwick, J. & Benson, M., Mar 16 2017, In : Amyloid. 24, p. 95-96 2 p.

Research output: Contribution to journalLetter

Assessing mNIS+7Ionis and international neurologists' proficiency in a familial amyloidotic polyneuropathy trial

Dyck, P. J., Kincaid, J. C., Dyck, P. J. B., Chaudhry, V., Goyal, N. A., Alves, C., Salhi, H., Wiesman, J. F., Labeyrie, C., Robinson-Papp, J., Cardoso, M., Laura, M., Ruzhansky, K., Cortese, A., Brannagan, T. H., Khoury, J., Khella, S., Waddington-Cruz, M., Ferreira, J., Wang, A. K. & 24 others, Pinto, M. V., Ayache, S. S., Benson, M. D., Berk, J. L., Coelho, T., Polydefkis, M., Gorevic, P., Adams, D. H., Plante-Bordeneuve, V., Whelan, C., Merlini, G., Heitner, S., Drachman, B. M., Conceição, I., Klein, C. J., Gertz, M. A., Ackermann, E. J., Hughes, S. G., Mauermann, M. L., Bergemann, R., Lodermeier, K. A., Davies, J. L., Carter, R. E. & Litchy, W. J., Nov 2017, In : Muscle and Nerve. 56, 5, p. 901-911 11 p.

Research output: Contribution to journalArticle

23 Scopus citations

Familial wild-type transthyretin cardiomyopathy

Benson, M., Berk, J. L., Connors, L. H. & Dasgupta, N., Mar 16 2017, In : Amyloid. 24, p. 91-92 2 p.

Research output: Contribution to journalLetter

Insulin: a diagnostic warning

Liepnieks, J. J., Benson, M. & Kluve-Beckerman, B., Mar 16 2017, In : Amyloid. 24, p. 159-160 2 p.

Research output: Contribution to journalLetter

24 Scopus citations

Transthyretin amyloidosis: a little history of hereditary amyloidosis

Benson, M., Mar 16 2017, In : Amyloid. 24, p. 76-77 2 p.

Research output: Contribution to journalLetter

2 Scopus citations

Treatment of transthyretin cardiomyopathy with a TTR-specific antisense oligonucleotide (IONIS-TTRRx)

Benson, M., Ackermann, E. J. & Monia, B. P., Mar 16 2017, In : Amyloid. 24, p. 134-135 2 p.

Research output: Contribution to journalLetter

7 Scopus citations
2016

Amyloid Cardiomyopathy

Benson, M. & Dasgupta, N., Jul 5 2016, In : Journal of the American College of Cardiology. 68, 1, p. 25-28 4 p.

Research output: Contribution to journalComment/debate

3 Scopus citations

Amyloid fibril proteins and amyloidosis: chemical identification and clinical classification International Society of Amyloidosis 2016 Nomenclature Guidelines

Sipe, J. D., Benson, M., Buxbaum, J. N., Ikeda, S. I., Merlini, G., Saraiva, M. J. M. & Westermark, P., Oct 1 2016, In : Amyloid. 23, 4, p. 209-213 5 p.

Research output: Contribution to journalArticle

229 Scopus citations

Biochemical characterization of vitreous amyloid formed after liver transplantation

Liepnieks, J. J., Phan, A-D., Wise, R. J., Hrisomalos, F. N. & Benson, M., Apr 1 2016, (Accepted/In press) In : Amyloid. p. 1-2 2 p.

Research output: Contribution to journalArticle

1 Scopus citations

Carbamylation of the amino-terminal residue (Gly1) of mouse serum amyloid A promotes amyloid formation in a cell culture model

Kluve-Beckerman, B., Liepnieks, J. J., Benson, M., Lai, X., Qi, G. & Wang, M., Dec 1 2016, In : FEBS Letters. 590, 23, p. 4296-4307 12 p.

Research output: Contribution to journalLetter

4 Scopus citations

Disease-free survival following high dose or standard dose therapy in patients with amyloidosis

Kiel, P. J., Trueg, A. O., Ferguson, M., Benson, M. & Abonour, R., Jul 1 2016, In : British journal of haematology. 174, 1, p. 153-155 3 p.

Research output: Contribution to journalLetter

3 Scopus citations

Liver transplant alone without kidney transplant for fibrinogen Aα-chain (AFib) renal amyloidosis

Fix, O. K., Stock, P. G., Lee, B. K. & Benson, M. D., Apr 2 2016, In : Amyloid. 23, 2, p. 132-133 2 p.

Research output: Contribution to journalLetter

2 Scopus citations

Suppressing transthyretin production in mice, monkeys and humans using 2nd-Generation antisense oligonucleotides

Ackermann, E. J., Guo, S., Benson, M., Booten, S., Freier, S., Hughes, S. G., Kim, T. W., Jesse Kwoh, T., Matson, J., Norris, D., Yu, R., Watt, A. & Monia, B. P., Jun 17 2016, (Accepted/In press) In : Amyloid. p. 1-10 10 p.

Research output: Contribution to journalArticle

55 Scopus citations