Arrhythmias in the Muscular Dystrophies

Archana Rajdev, William Groh

Research output: Contribution to journalArticle

6 Citations (Scopus)

Abstract

In patients with muscular dystrophies, cardiac involvement leading to cardiomyopathy and arrhythmias occurs with variable prevalence, mirroring the phenotypic variability seen among and within the various hereditary myopathies. Knowledge of the incidence of arrhythmias and predictors of sudden death in the various hereditary myopathies can help guide screening and appropriate management of these patients, thereby improving survival. The noncardiac manifestations can lead to delayed recognition of symptoms, affect the decision to implant a prophylactic device, and once a decision is made to proceed with device implant, increase peri-procedural respiratory and anesthesia-related complications.

Original languageEnglish (US)
Pages (from-to)303-308
Number of pages6
JournalCardiac Electrophysiology Clinics
Volume7
Issue number2
DOIs
StatePublished - Jun 1 2015
Externally publishedYes

Fingerprint

Muscular Dystrophies
Muscular Diseases
Cardiac Arrhythmias
Equipment and Supplies
Sudden Death
Cardiomyopathies
Anesthesia
Survival
Incidence

Keywords

  • Arrhythmia
  • Genetics
  • Implantable cardioverter-defibrillator
  • Muscular dystrophy
  • Pacemaker
  • Sudden cardiac death

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Physiology (medical)

Cite this

Arrhythmias in the Muscular Dystrophies. / Rajdev, Archana; Groh, William.

In: Cardiac Electrophysiology Clinics, Vol. 7, No. 2, 01.06.2015, p. 303-308.

Research output: Contribution to journalArticle

Rajdev, Archana ; Groh, William. / Arrhythmias in the Muscular Dystrophies. In: Cardiac Electrophysiology Clinics. 2015 ; Vol. 7, No. 2. pp. 303-308.
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