Cochlear implantation for hearing loss associated with bilateral endolymphatic sac tumors in von Hippel-Lindau disease

Jay Jagannathan, Russell R. Lonser, Richard A. Stanger, John A. Butman, Alexander Vortmeyer, Christopher K. Zalewski, Carmen Brewer, Christal Surowicz, H. Jeffrey Kim

Research output: Contribution to journalArticle

8 Citations (Scopus)

Abstract

OBJECTIVE: Bilateral endolymphatic sac tumors (ELSTs) are associated with von Hippel-Lindau disease and often underlie significant audiovestibular morbidity, including hearing loss. PATIENT: This 44-year-old female von Hippel-Lindau disease patient presented with tinnitus, vertigo, and binaural hearing loss. Magnetic resonance and computed tomography imaging demonstrated bilateral ELSTs, and audiometry confirmed bilateral hearing loss. INTERVENTION: The patient underwent staged resection of the ELSTs (left then right). After resection of the left ELST and during the same operation, a cochlear implant was placed. MAIN OUTCOME MEASURES: Clinical, audiometric, and imaging data. RESULTS: Postoperatively, the patient had resolution of tinnitus and vertigo with a significant implant-aided improvement in hearing. CONCLUSION: Because of their unique anatomic and biologic features, resection of bilateral tumors and cochlear implantation in deaf ELST patients is a potential option to improve hearing and quality of life.

Original languageEnglish (US)
Pages (from-to)927-930
Number of pages4
JournalOtology and Neurotology
Volume28
Issue number7
DOIs
StatePublished - Oct 1 2007
Externally publishedYes

Fingerprint

Endolymphatic Sac
von Hippel-Lindau Disease
Cochlear Implantation
Sensorineural Hearing Loss
Neoplasms
Tinnitus
Vertigo
Hearing Loss
Hearing
Bilateral Hearing Loss
Audiometry
Cochlear Implants
Magnetic Resonance Spectroscopy
Tomography
Quality of Life
Morbidity

Keywords

  • Bilateral
  • Cochlear implant
  • Endolymphatic sac tumor
  • Hearing loss
  • Von Hippel-Lindau disease

ASJC Scopus subject areas

  • Otorhinolaryngology
  • Sensory Systems
  • Clinical Neurology

Cite this

Cochlear implantation for hearing loss associated with bilateral endolymphatic sac tumors in von Hippel-Lindau disease. / Jagannathan, Jay; Lonser, Russell R.; Stanger, Richard A.; Butman, John A.; Vortmeyer, Alexander; Zalewski, Christopher K.; Brewer, Carmen; Surowicz, Christal; Kim, H. Jeffrey.

In: Otology and Neurotology, Vol. 28, No. 7, 01.10.2007, p. 927-930.

Research output: Contribution to journalArticle

Jagannathan, J, Lonser, RR, Stanger, RA, Butman, JA, Vortmeyer, A, Zalewski, CK, Brewer, C, Surowicz, C & Kim, HJ 2007, 'Cochlear implantation for hearing loss associated with bilateral endolymphatic sac tumors in von Hippel-Lindau disease', Otology and Neurotology, vol. 28, no. 7, pp. 927-930. https://doi.org/10.1097/MAO.0b013e31805c7506
Jagannathan, Jay ; Lonser, Russell R. ; Stanger, Richard A. ; Butman, John A. ; Vortmeyer, Alexander ; Zalewski, Christopher K. ; Brewer, Carmen ; Surowicz, Christal ; Kim, H. Jeffrey. / Cochlear implantation for hearing loss associated with bilateral endolymphatic sac tumors in von Hippel-Lindau disease. In: Otology and Neurotology. 2007 ; Vol. 28, No. 7. pp. 927-930.
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