Cochlear implantation in auditory neuropathy

Richard T. Miyamoto, Karen Iler Kirk, Julia Renshaw, Debra Hussain

Research output: Contribution to journalArticlepeer-review

121 Scopus citations


Objective: Auditory neuropathy is a recently described clinical entity characterized by sensorineural hearing loss in which the auditory evoked potential (ABR) is absent but otoacoustic emissions are present. This suggests a central locus for the associated hearing loss. In this study the results observed in a child with auditory neuropathy who received a cochlear implant are presented and compared with those of a matched group of children who were recipients of implants. Methods: A single-subject, repeated-measures design, evaluating closed-set and open-set word recognition abilities was used to assess the subject and a control group of matched children with implants who had also experienced a progressive sensorineural hearing loss. Results: The subject demonstrated improvements in vowel recognition (82% correct) by 1 year after implantation, which were only slightly lower than the control group. Consonant recognition and open-set word recognition scores were significantly lower. Conclusion: Caution should be exercised when considering cochlear implantation in children with auditory neuropathy. As with conventional hearing aids, less than optimal results may be seen.

Original languageEnglish (US)
Pages (from-to)181-185
Number of pages5
Issue number2
StatePublished - Feb 1999

ASJC Scopus subject areas

  • Otorhinolaryngology

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