Cranio-orbital-temporal neurofibromatosis: Are we treating the whole problem?

Robert J. Havlik, Joel Boaz

Research output: Contribution to journalArticle

21 Scopus citations

Abstract

Cranio-orbital-temporal neurofibromatosis is an uncommon subtype of neurofibromatosis 1 characterized by pulsatile exophthalmos, orbital neurofibromas, sphenoid wing dysplasia, expansion of the temporal fossa, and herniation of the temporal lobe into the orbit. The cause of the sphenoid wing dysplasia is uncertain. Reconstruction of the sphenoid defect, separating the orbit and cranial vault, has been problematic because of resorption of bone grafts. This reports illustrates one potential cause of the sphenoid defect and a possible cause of the bone graft resorption.

Original languageEnglish (US)
Pages (from-to)529-535
Number of pages7
JournalJournal of Craniofacial Surgery
Volume9
Issue number6
DOIs
StatePublished - Nov 1998

Keywords

  • Craniofacial
  • Neurofibromatosis
  • Orbit
  • Sphenoid skull base
  • Surgery

ASJC Scopus subject areas

  • Surgery

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