Emergencies in patients with inherited hemoglobin disorders - An emergency department perspective

Rebecca R. Hampton, Vinod Balasa, Sheryl Allen

Research output: Contribution to journalArticle

1 Citation (Scopus)

Abstract

Hemoglobin (Hb) disorders presenting to the emergency department (ED) can be a diagnostic and management problem if not properly recognized. It is important to understand the nomenclature and pathophysiology of these entities. Common Hb disorders presenting to the ED include sickle cell disease, thalassemias, and methemoglobinemia. Complications of sickle cell disease comprise the majority of illness from Hb disorders seen in the ED or outpatient setting. These complications include pain crisis, sepsis, acute chest syndrome, and cerebrovascular accidents. Rapid diagnosis and treatment are necessary to minimize morbidity and mortality. In a case-based format, the clinical presentation, assessment, and management of the above will be discussed to help clinicians practice in an evidence-based fashion.

Original languageEnglish (US)
Pages (from-to)138-148
Number of pages11
JournalClinical Pediatric Emergency Medicine
Volume6
Issue number3
DOIs
StatePublished - Sep 2005
Externally publishedYes

Fingerprint

Hospital Emergency Service
Hemoglobins
Emergencies
Sickle Cell Anemia
Acute Chest Syndrome
Methemoglobinemia
Thalassemia
Evidence-Based Practice
Terminology
Sepsis
Outpatients
Stroke
Morbidity
Pain
Mortality
Therapeutics

Keywords

  • Hemoglobin disorders
  • Methemoglobinemia
  • Sickle cell disease
  • Thalassemias

ASJC Scopus subject areas

  • Emergency Medicine
  • Pediatrics, Perinatology, and Child Health

Cite this

Emergencies in patients with inherited hemoglobin disorders - An emergency department perspective. / Hampton, Rebecca R.; Balasa, Vinod; Allen, Sheryl.

In: Clinical Pediatric Emergency Medicine, Vol. 6, No. 3, 09.2005, p. 138-148.

Research output: Contribution to journalArticle

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