Macroreentrant ventricular tachycardia and coronary artery disease in cerebrotendinous xanthomatosis

Peng Sheng Chen, R. Peter Fleck, Constance M. Calisi, Joseph A. Kozina, Gregory K. Feld

Research output: Contribution to journalArticle

4 Scopus citations

Abstract

Cerebrotendinous xanthomatosis, a metabolic lipid disorder characterized by a defect in the conversion of cholesterol into bile acids, is a rare disease with <100 cases reported.1 The His-Purkinje system macroreentrant ventricular tachycardia (VT) is an uncommon arrhythmia, and accounts for the underlying mechanism in approximately 6% of induced sustained monomorphic VT.2,3 We herein describe a patient with cerebrotendinous xanthomatosis, a history of sudden cardiac death and 2 morphologies of VT due to 2 different mechanisms.

Original languageEnglish (US)
Pages (from-to)680-682
Number of pages3
JournalThe American journal of cardiology
Volume64
Issue number10
DOIs
StatePublished - Sep 15 1989
Externally publishedYes

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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