Neurologic presentation of Erdheim-Chester disease

Cynthia Bodkin, Zbigniew K. Wszolek

Research output: Contribution to journalArticle

11 Citations (Scopus)

Abstract

Erdheim-Chester disease is a rare, systemic histiocytosis that involves multiple organ systems and causes symmetric sclerosis of the metaphysis and diaphysis of the long bones. We present 2 cases and reviewed 108 patients reported in the literature who had neurologic manifestations of Erdheim - Chester disease. After eye involvement or diabetes insipidus, cerebellar symptoms were most frequently encountered, followed by tumor, headaches, cord compression, mental status change, seizures, and change in libido. A wide range of neurological symptoms can be seen in ECD. Therefore we hope the review brings more awareness about this disorder.

Original languageEnglish (US)
Pages (from-to)397-403
Number of pages7
JournalNeurologia i Neurochirurgia Polska
Volume40
Issue number5
StatePublished - 2006
Externally publishedYes

Fingerprint

Erdheim-Chester Disease
Nervous System
Histiocytosis
Libido
Diaphyses
Diabetes Insipidus
Sclerosis
Neurologic Manifestations
Headache
Seizures
Bone and Bones
Neoplasms

Keywords

  • Erdheim-Chester disease
  • Neurological symptoms
  • Non-Langerhans histiocytosis

ASJC Scopus subject areas

  • Clinical Neurology
  • Neurology

Cite this

Neurologic presentation of Erdheim-Chester disease. / Bodkin, Cynthia; Wszolek, Zbigniew K.

In: Neurologia i Neurochirurgia Polska, Vol. 40, No. 5, 2006, p. 397-403.

Research output: Contribution to journalArticle

Bodkin, Cynthia ; Wszolek, Zbigniew K. / Neurologic presentation of Erdheim-Chester disease. In: Neurologia i Neurochirurgia Polska. 2006 ; Vol. 40, No. 5. pp. 397-403.
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