Orthopedic aspects of rett syndrome

A multicenter review

Randall Loder, Christopher L. Lee, B. Stephens Richards

Research output: Contribution to journalArticle

22 Citations (Scopus)

Abstract

Twenty-three of 36 patients (64%) with Rett syndrome showed orthopedic problems at an average age of 8 years 7 months. Sixteen patients had spinal deformities (45%), six had scoliosis, one had sagittal deformity, and nine had scoliosis with sagittal deformity. Eight patients with scoliosis have shown progression, with two patients requiring surgery. Thirteen patients (36%) exhibited joint contractures; three of them have required surgery. Ten fractures occurred in five patients (14%). Coxa valga was present in all 14 hips. Skeletal ages in four preadolescent patients were normal.

Original languageEnglish (US)
Pages (from-to)557-562
Number of pages6
JournalJournal of Pediatric Orthopaedics
Volume9
Issue number5
StatePublished - 1989
Externally publishedYes

Fingerprint

Rett Syndrome
Orthopedics
Scoliosis
Coxa Valga
Contracture
Hip
Joints

Keywords

  • Coxa valga
  • Fractures
  • Joint contractures
  • Rett syndrome
  • Spinal deformities

ASJC Scopus subject areas

  • Orthopedics and Sports Medicine
  • Pediatrics, Perinatology, and Child Health
  • Surgery

Cite this

Orthopedic aspects of rett syndrome : A multicenter review. / Loder, Randall; Lee, Christopher L.; Richards, B. Stephens.

In: Journal of Pediatric Orthopaedics, Vol. 9, No. 5, 1989, p. 557-562.

Research output: Contribution to journalArticle

Loder, Randall ; Lee, Christopher L. ; Richards, B. Stephens. / Orthopedic aspects of rett syndrome : A multicenter review. In: Journal of Pediatric Orthopaedics. 1989 ; Vol. 9, No. 5. pp. 557-562.
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