Persistent Sweet's syndrome occurring in a child with a primary immunodeficiency

Kimberly E. Lipp, Philip D. Shenefelt, Robert P. Nelson, Jane L. Messina, Neil A. Fenske

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Abstract

Sweet's syndrome (SS) occurs most commonly in association with inflammatory or neoplastic disorders. Only rarely has it been associated with immunodeficiency disorders. We describe a child with a T-cell immunodeficiency who had a persistent neutrophilic dermatosis that was histologically and clinically consistent with SS. SS associated with immunodeficiencies may occur as a reaction to an underlying infection or a defect in immunoregulation. Such patients, however, may not be able to produce the classic fever and neutrophilia associated with SS. They may fail to respond to standard treatment for SS and may suffer a prolonged and persistent course.

Original languageEnglish (US)
Pages (from-to)838-841
Number of pages4
JournalJournal of the American Academy of Dermatology
Volume40
Issue number5 SUPPL. 1
DOIs
StatePublished - Jan 1 1999

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ASJC Scopus subject areas

  • Dermatology

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