Persistent sweet's syndrome occurring in a child with a primary immunodeficiency

K. E. Lipp, P. D. Shenefelt, Robert Nelson, J. L. Messina, N. A. Fenske

Research output: Contribution to journalArticle

23 Citations (Scopus)

Abstract

Sweet's syndrome (SS) occurs most commonly in association with inflammatory or neoplastic disorders. Only rarely has it been associated with immunodeficiency disorders. We describe a child with a T-cell immunodeficiency who had a persistent neutrophilic dermatosis that was histologically and clinically consistent with SS. SS associated with immunodeficiencies may occur as a reaction to an underlying infection or a defect in immunoregulation. Such patients, however, may not be able to produce the classic fever and neutrophilia associated with SS. They may fail to respond to standard treatment for SS and may suffer a prolonged and persistent course.

Original languageEnglish (US)
Pages (from-to)838-841
Number of pages4
JournalJournal of the American Academy of Dermatology
Volume40
Issue number5 II
DOIs
StatePublished - 1999
Externally publishedYes

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Sweet Syndrome
Skin Diseases
Fever
T-Lymphocytes
Infection

ASJC Scopus subject areas

  • Dermatology

Cite this

Persistent sweet's syndrome occurring in a child with a primary immunodeficiency. / Lipp, K. E.; Shenefelt, P. D.; Nelson, Robert; Messina, J. L.; Fenske, N. A.

In: Journal of the American Academy of Dermatology, Vol. 40, No. 5 II, 1999, p. 838-841.

Research output: Contribution to journalArticle

Lipp, K. E. ; Shenefelt, P. D. ; Nelson, Robert ; Messina, J. L. ; Fenske, N. A. / Persistent sweet's syndrome occurring in a child with a primary immunodeficiency. In: Journal of the American Academy of Dermatology. 1999 ; Vol. 40, No. 5 II. pp. 838-841.
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