Persistent Sweet's syndrome occurring in a child with a primary immunodeficiency

Kimberly E. Lipp, Philip D. Shenefelt, Robert P. Nelson, Jane L. Messina, Neil A. Fenske

Research output: Contribution to journalArticle

23 Scopus citations


Sweet's syndrome (SS) occurs most commonly in association with inflammatory or neoplastic disorders. Only rarely has it been associated with immunodeficiency disorders. We describe a child with a T-cell immunodeficiency who had a persistent neutrophilic dermatosis that was histologically and clinically consistent with SS. SS associated with immunodeficiencies may occur as a reaction to an underlying infection or a defect in immunoregulation. Such patients, however, may not be able to produce the classic fever and neutrophilia associated with SS. They may fail to respond to standard treatment for SS and may suffer a prolonged and persistent course.

Original languageEnglish (US)
Pages (from-to)838-841
Number of pages4
JournalJournal of the American Academy of Dermatology
Issue number5 SUPPL. 1
StatePublished - Jan 1 1999
Externally publishedYes

ASJC Scopus subject areas

  • Dermatology

Fingerprint Dive into the research topics of 'Persistent Sweet's syndrome occurring in a child with a primary immunodeficiency'. Together they form a unique fingerprint.

  • Cite this