Primary Spinal Intradural Extraosseous Ewing Sarcoma in a Pediatric Patient: Case Report and Review of the Literature

Joshua T. Scantland, Mercia J. Gondim, Andrew S. Koivuniemi, Daniel H. Fulkerson, Chie Schin Shih

Research output: Contribution to journalArticle

2 Scopus citations

Abstract

Ewing sarcoma (ES) is an aggressive, primary bone malignancy with occasional soft tissue extension. Purely extra-osseous ES is rare. A primary intraspinal, intradural ES without bone involvement is exceedingly rare. ES may be differentiated from other primitive neuroectodermal tumors by molecular analysis. The authors report the case of a 14-year-old female who suffered an acute neurologic decline from a hemorrhagic, intraspinal, intradural ES. The patient has been tumor free for 2 years after the initial emergency surgery. Our management of the patient and a review of the literature are provided. Considering only those cases with molecular or genetic confirmation of ES, our patient is the fifth pediatric case reported in the English literature.

Original languageEnglish (US)
Pages (from-to)222-228
Number of pages7
JournalPediatric Neurosurgery
Volume53
Issue number4
DOIs
StatePublished - Jun 1 2018

Keywords

  • Ewing sarcoma
  • Extraosseous sarcoma
  • Intradural sarcoma
  • Intraspinal sarcoma
  • Pediatric surgery
  • Spine

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Surgery
  • Clinical Neurology

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