Resolution of acquired pulmonary arteriovenous malformations in a patient with total anomalous systemic venous return

Tiffanie Johnson, M. S. Schamberger, John Brown, D. A. Girod

Research output: Contribution to journalArticle

11 Citations (Scopus)

Abstract

An 11-year-old male with total anomalous systemic venous return had surgical repair except for the hepatic venous return, which drained to the left atrium. He developed progressive cyanosis and fatigue and was diagnosed with large pulmonary arteriovenous malformations (PAVMs) during cardiac catheterization with the use of bubble contrast echocardiography. After surgical redirection of hepatic venous flow to the right heart and pulmonary arterial system, resolution of these PAVMs was demonstrated clinically and by contrast echocardiography. This unique case report demonstrates the development of PAVMs with exclusion of hepatic venous return through the pulmonary vascular bed while pulsatile pulmonary blood flow remains intact. It reinforces the likelihood of the absence of an as yet unidentified hepatic vasoactive substance as the source for development of PAVMs.

Original languageEnglish
Pages (from-to)210-212
Number of pages3
JournalPediatric Cardiology
Volume23
Issue number2
DOIs
StatePublished - Mar 2002

Fingerprint

Arteriovenous Malformations
Lung
Liver
Echocardiography
Cyanosis
Cardiac Catheterization
Heart Atria
Fatigue
Blood Vessels

Keywords

  • Arteriovenous fistula
  • Cavopulmonary anastomosis
  • Congenital heart disease
  • Contrast echocardiography
  • Pulmonary arteriovenous fistula
  • Pulmonary circulation

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine
  • Pediatrics, Perinatology, and Child Health

Cite this

Resolution of acquired pulmonary arteriovenous malformations in a patient with total anomalous systemic venous return. / Johnson, Tiffanie; Schamberger, M. S.; Brown, John; Girod, D. A.

In: Pediatric Cardiology, Vol. 23, No. 2, 03.2002, p. 210-212.

Research output: Contribution to journalArticle

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