Retroperitoneal xanthogranuloma in a patient with Erdheim-Chester disease

John Eble, A. E. Rosenberg, R. H. Young

Research output: Contribution to journalArticle

44 Citations (Scopus)

Abstract

A case of Erdheim-Chester disease with retroperitoneal and renal sinus xanthogranuloma that occurred in a 50-year-old woman is presented. The 12 previously reported cases of Erdheim-Chester disease associated with retroperitoneal xanthogranuloma are reviewed and compared with 13 sporadic cases of retroperitoneal xanthogranuloma. Retroperitoneal xanthogranuloma is distinguished from inflammatory malignant fibrous histiocytoma by its lack of neutrophils, inconspicuous vascularity, lack of nuclear atypia, and abundant collagen. It is distinguished from inflammatory fibrosarcoma by its numerous foamy histiocytes, relative lack of plasma cells, and lack of nuclear atypia; it is distinguished from retroperitoneal fibrosis principally by its many foamy histiocytes, lack of plasma cells, and lack of vasculitis.

Original languageEnglish (US)
Pages (from-to)843-848
Number of pages6
JournalAmerican Journal of Surgical Pathology
Volume18
Issue number8
StatePublished - 1994
Externally publishedYes

Fingerprint

Erdheim-Chester Disease
Histiocytes
Plasma Cells
Retroperitoneal Fibrosis
Malignant Fibrous Histiocytoma
Fibrosarcoma
Vasculitis
Neutrophils
Collagen
Kidney

ASJC Scopus subject areas

  • Anatomy
  • Pathology and Forensic Medicine

Cite this

Retroperitoneal xanthogranuloma in a patient with Erdheim-Chester disease. / Eble, John; Rosenberg, A. E.; Young, R. H.

In: American Journal of Surgical Pathology, Vol. 18, No. 8, 1994, p. 843-848.

Research output: Contribution to journalArticle

@article{83f1a625eb0444fd87656bb022f8f829,
title = "Retroperitoneal xanthogranuloma in a patient with Erdheim-Chester disease",
abstract = "A case of Erdheim-Chester disease with retroperitoneal and renal sinus xanthogranuloma that occurred in a 50-year-old woman is presented. The 12 previously reported cases of Erdheim-Chester disease associated with retroperitoneal xanthogranuloma are reviewed and compared with 13 sporadic cases of retroperitoneal xanthogranuloma. Retroperitoneal xanthogranuloma is distinguished from inflammatory malignant fibrous histiocytoma by its lack of neutrophils, inconspicuous vascularity, lack of nuclear atypia, and abundant collagen. It is distinguished from inflammatory fibrosarcoma by its numerous foamy histiocytes, relative lack of plasma cells, and lack of nuclear atypia; it is distinguished from retroperitoneal fibrosis principally by its many foamy histiocytes, lack of plasma cells, and lack of vasculitis.",
author = "John Eble and Rosenberg, {A. E.} and Young, {R. H.}",
year = "1994",
language = "English (US)",
volume = "18",
pages = "843--848",
journal = "American Journal of Surgical Pathology",
issn = "0147-5185",
publisher = "Lippincott Williams and Wilkins",
number = "8",

}

TY - JOUR

T1 - Retroperitoneal xanthogranuloma in a patient with Erdheim-Chester disease

AU - Eble, John

AU - Rosenberg, A. E.

AU - Young, R. H.

PY - 1994

Y1 - 1994

N2 - A case of Erdheim-Chester disease with retroperitoneal and renal sinus xanthogranuloma that occurred in a 50-year-old woman is presented. The 12 previously reported cases of Erdheim-Chester disease associated with retroperitoneal xanthogranuloma are reviewed and compared with 13 sporadic cases of retroperitoneal xanthogranuloma. Retroperitoneal xanthogranuloma is distinguished from inflammatory malignant fibrous histiocytoma by its lack of neutrophils, inconspicuous vascularity, lack of nuclear atypia, and abundant collagen. It is distinguished from inflammatory fibrosarcoma by its numerous foamy histiocytes, relative lack of plasma cells, and lack of nuclear atypia; it is distinguished from retroperitoneal fibrosis principally by its many foamy histiocytes, lack of plasma cells, and lack of vasculitis.

AB - A case of Erdheim-Chester disease with retroperitoneal and renal sinus xanthogranuloma that occurred in a 50-year-old woman is presented. The 12 previously reported cases of Erdheim-Chester disease associated with retroperitoneal xanthogranuloma are reviewed and compared with 13 sporadic cases of retroperitoneal xanthogranuloma. Retroperitoneal xanthogranuloma is distinguished from inflammatory malignant fibrous histiocytoma by its lack of neutrophils, inconspicuous vascularity, lack of nuclear atypia, and abundant collagen. It is distinguished from inflammatory fibrosarcoma by its numerous foamy histiocytes, relative lack of plasma cells, and lack of nuclear atypia; it is distinguished from retroperitoneal fibrosis principally by its many foamy histiocytes, lack of plasma cells, and lack of vasculitis.

UR - http://www.scopus.com/inward/record.url?scp=0028364868&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=0028364868&partnerID=8YFLogxK

M3 - Article

VL - 18

SP - 843

EP - 848

JO - American Journal of Surgical Pathology

JF - American Journal of Surgical Pathology

SN - 0147-5185

IS - 8

ER -