The congenital porto-caval fistula: A unique presentation and novel intervention

Wynton Hoover, Veda Ackerman, Marcus Schamberger, Manjusha Kumar, Francis Marshalleck, Mark Hoyer

Research output: Contribution to journalArticle

6 Citations (Scopus)

Abstract

Congenital porto-caval tistulas are uncommon vascular malformations with a varied clinical presentation beginning in intancy and spanning late adulthood. We report a 14-year-old male who presented with dyspnea and cough. His past medical history was signiticant tor a chronic non-immune hemolytic anemia, thrombocytopenia, coagulopathy and a learning disability. He was found to have severe pulmonary hypertension and hyperammonemia associated with a large congenital porto-caval tistula. The abnormal vessel was occluded via endovascular covered stent placement in the vena cava. His pulmonary hypertension has improved remarkably while his chronic anemia, thrombocytopenia and ammonia have normalized to allow improved cognitive performance.

Original languageEnglish
Pages (from-to)196-199
Number of pages4
JournalPediatric Pulmonology
Volume43
Issue number2
DOIs
StatePublished - Feb 2008

Fingerprint

Venae Cavae
Fistula
Pulmonary Hypertension
Thrombocytopenia
Hyperammonemia
Vascular Malformations
Learning Disorders
Hemolytic Anemia
Ammonia
Cough
Dyspnea
Stents
Anemia

Keywords

  • Abernethy malformation
  • Congenital porto-caval fistula
  • Hemolytic anemia
  • Hyperammonemia
  • Portosystemic shunt
  • Pulmonary hypertension

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Pulmonary and Respiratory Medicine

Cite this

The congenital porto-caval fistula : A unique presentation and novel intervention. / Hoover, Wynton; Ackerman, Veda; Schamberger, Marcus; Kumar, Manjusha; Marshalleck, Francis; Hoyer, Mark.

In: Pediatric Pulmonology, Vol. 43, No. 2, 02.2008, p. 196-199.

Research output: Contribution to journalArticle

Hoover, W, Ackerman, V, Schamberger, M, Kumar, M, Marshalleck, F & Hoyer, M 2008, 'The congenital porto-caval fistula: A unique presentation and novel intervention', Pediatric Pulmonology, vol. 43, no. 2, pp. 196-199. https://doi.org/10.1002/ppul.20727
Hoover, Wynton ; Ackerman, Veda ; Schamberger, Marcus ; Kumar, Manjusha ; Marshalleck, Francis ; Hoyer, Mark. / The congenital porto-caval fistula : A unique presentation and novel intervention. In: Pediatric Pulmonology. 2008 ; Vol. 43, No. 2. pp. 196-199.
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