This report describes a 7-year-old boy presenting with watery diarrhea, hypokalemia, and hypochlohydria associated with vasoactive intestinal polypeptide (VIP)-secreting ganglioneuromatosis involving the entire colon and rectum. The child's symptoms resolved following proctocolectomy, and the VIP levels returned to normal. Although 55 previous children have been reported with VIP-secreting tumors, this case is the first involving the entire colon and recturm.
- achlorhydria syndrome (WDHA)
- Intestinal ganglioneuroma
- vasoactive intestinal polypeptide (VIP)
- watery diarrhea
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health