Vasoactive intestinal polypeptide-secreting ganglioneuromatosis affecting the entire colon and rectum

Frederick J. Rescorla, Dennis W. Vane, Joseph F. Fitzgerald, Karen W. West, Jay L. Grosfeld

Research output: Contribution to journalArticlepeer-review

25 Scopus citations

Abstract

This report describes a 7-year-old boy presenting with watery diarrhea, hypokalemia, and hypochlohydria associated with vasoactive intestinal polypeptide (VIP)-secreting ganglioneuromatosis involving the entire colon and rectum. The child's symptoms resolved following proctocolectomy, and the VIP levels returned to normal. Although 55 previous children have been reported with VIP-secreting tumors, this case is the first involving the entire colon and recturm.

Original languageEnglish (US)
Pages (from-to)635-637
Number of pages3
JournalJournal of Pediatric Surgery
Volume23
Issue number7
DOIs
StatePublished - Jul 1988
Externally publishedYes

Keywords

  • achlorhydria syndrome (WDHA)
  • hypokalemia
  • Intestinal ganglioneuroma
  • vasoactive intestinal polypeptide (VIP)
  • watery diarrhea

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Surgery

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